Anesthetic Management of a Patient with Poland’s syndrome: A Case Report
##plugins.themes.bootstrap3.article.main##
Poland syndrome is a rare congenital disease characterized by various degrees of chest wall defects, such as deficits in the small thoracic muscle and defects in the neuromuscular region of the small thoracic muscle. In addition, this condition may present with loss or weak development of the papilla and breasts and can be accompanied by brachydactyly, syndactyly, and limb defects in the hands and feet on the same side. Poland syndrome also may cause various deformities in the heart, lungs, and kidneys. These lung deformities can produce hypoventilation and hypoxia as the function of the respiratory muscle decreases, leading to increased pulmonary complications postoperatively. Since these patients also have an increased risk of malignant hyperthermia, careful attention is required in the selection of drugs for inducing general anesthesia. We would like to report an experience of general anesthesia for breast reconstruction in a 20-year-old female patient with Poland syndrome.
Downloads
References
-
Fokin AA, Robicsek F: Poland's syndrome revisited. The Annals of Thoracic Surgery. 2002; 74(6): 2218-25.
DOI | Google Scholar
1
-
Romanini MV, Calevo MG, Puliti A, Vaccari C, Valle M, Senes F, Torre M: Poland syndrome: A proposed classification system and perspectives on diagnosis and treatment. Semin Pediatr Surg. 2018; 27(3): 189-99.
DOI | Google Scholar
2
-
Küpper HJ: Anesthesia in Poland syndrome. Canadian journal of anaesthesia = Journal canadien d'anesthesie. 1999; 46(5 Pt 1): 513-514.
DOI | Google Scholar
3
-
Cordero García C, Nieto Castilla A, López Jiménez E, Amores García I: Dextrocardia associated with left-sided Poland syndrome. American Journal of Physical Medicine & Rehabilitation. 2009; 88(2): 168.
DOI | Google Scholar
4
-
Aslan D, Balci S: Temporary dysplastic hematological features due to iron deficiency in a case of Poland syndrome. Pediatric Hematology and Oncology. 2004; 21(8):711-5.
DOI | Google Scholar
5
-
Merlob P, Schonfeld A, Ovadia Y, Reisner SH: Real-time echo-Doppler Duplex Scanner in the evaluation of patients with Poland sequence. European Journal of Obstetrics, Gynecology, and Reproductive Biology. 1989; 32(2): 103-8.
DOI | Google Scholar
6
-
Rosenberg H, Pollock N, Schiemann A, Bulger T, Stowell K: Malignant hyperthermia: a review. Orphanet Journal of Rare Diseases. 2015; 10: 93.
DOI | Google Scholar
7
-
Riazi S, Kraeva N, Hopkins PM: Updated guide for the management of malignant hyperthermia. Canadian Journal of Anaesthesia. 2018; 65(6): 709-21.
DOI | Google Scholar
8